Cystic Fibrosis

Rescue by elexacaftor-tezacaftor-ivacaftor of the G1244E cystic fibrosis mutation's stability and gating defects are dependent on cell background

Wed, 2022-12-21 06:00

J Cyst Fibros. 2022 Dec 19:S1569-1993(22)01425-4. doi: 10.1016/j.jcf.2022.12.005. Online ahead of print.

NO ABSTRACT

PMID:36543707 | DOI:10.1016/j.jcf.2022.12.005

Categories: Literature Watch

Optic nerve sheath diameter correlates to intracranial pressure in spontaneous CSF leak patients

Wed, 2022-12-21 06:00

Int Forum Allergy Rhinol. 2022 Dec 21. doi: 10.1002/alr.23120. Online ahead of print.

NO ABSTRACT

PMID:36541893 | DOI:10.1002/alr.23120

Categories: Literature Watch

Computationally Efficient Assembly of Pseudomonas aeruginosa Gene Expression Compendia

Wed, 2022-12-21 06:00

mSystems. 2022 Dec 21:e0034122. doi: 10.1128/msystems.00341-22. Online ahead of print.

NO ABSTRACT

PMID:36541761 | DOI:10.1128/msystems.00341-22

Categories: Literature Watch

Pro-resolving and pro-inflammatory fatty acid-derived mediators in sputum of stable state bronchiectasis patients

Tue, 2022-12-20 06:00

Respir Res. 2022 Dec 20;23(1):363. doi: 10.1186/s12931-022-02301-5.

NO ABSTRACT

PMID:36539829 | DOI:10.1186/s12931-022-02301-5

Categories: Literature Watch

Nationwide survey of refractory asthma with bronchiectasis by inflammatory subtypes

Tue, 2022-12-20 06:00

Respir Res. 2022 Dec 20;23(1):365. doi: 10.1186/s12931-022-02289-y.

NO ABSTRACT

PMID:36539765 | DOI:10.1186/s12931-022-02289-y

Categories: Literature Watch

Insights into the molecular basis of c-di-GMP signalling in <em>Pseudomonas aeruginosa</em>

Tue, 2022-12-20 06:00

Crit Rev Microbiol. 2022 Dec 20:1-19. doi: 10.1080/1040841X.2022.2154140. Online ahead of print.

NO ABSTRACT

PMID:36539391 | DOI:10.1080/1040841X.2022.2154140

Categories: Literature Watch

ISPAD Clinical Practice Consensus Guidelines 2022: Management of cystic fibrosis-related diabetes in children and adolescents

Tue, 2022-12-20 06:00

Pediatr Diabetes. 2022 Dec;23(8):1212-1228. doi: 10.1111/pedi.13453.

NO ABSTRACT

PMID:36537525 | DOI:10.1111/pedi.13453

Categories: Literature Watch

The value of bronchocele attenuation in pulmonary computed tomography in assessment of allergic bronchopulmonary aspergillosis in the background of cystic fibrosis: A cross-sectional study

Tue, 2022-12-20 06:00

Ann Med Surg (Lond). 2022 Nov 17;84:104892. doi: 10.1016/j.amsu.2022.104892. eCollection 2022 Dec.

NO ABSTRACT

PMID:36536699 | PMC:PMC9758355 | DOI:10.1016/j.amsu.2022.104892

Categories: Literature Watch

Exercise and Airway Clearance Techniques in Cystic Fibrosis

Mon, 2022-12-19 06:00

Semin Respir Crit Care Med. 2022 Dec 19. doi: 10.1055/s-0042-1758729. Online ahead of print.

NO ABSTRACT

PMID:36535668 | DOI:10.1055/s-0042-1758729

Categories: Literature Watch

CFTR Modulators: Current Status and Evolving Knowledge

Mon, 2022-12-19 06:00

Semin Respir Crit Care Med. 2022 Dec 19. doi: 10.1055/s-0042-1758851. Online ahead of print.

NO ABSTRACT

PMID:36535667 | DOI:10.1055/s-0042-1758851

Categories: Literature Watch

Impact of Digital Technologies on Clinical Care for Adults with Cystic Fibrosis

Mon, 2022-12-19 06:00

Semin Respir Crit Care Med. 2022 Dec 19. doi: 10.1055/s-0042-1758730. Online ahead of print.

NO ABSTRACT

PMID:36535666 | DOI:10.1055/s-0042-1758730

Categories: Literature Watch

Antimicrobial Strategies for Cystic Fibrosis

Mon, 2022-12-19 06:00

Semin Respir Crit Care Med. 2022 Dec 19. doi: 10.1055/s-0042-1758733. Online ahead of print.

NO ABSTRACT

PMID:36535665 | DOI:10.1055/s-0042-1758733

Categories: Literature Watch

Beyond the Lungs-Emerging Challenges in Adult Cystic Fibrosis Care

Mon, 2022-12-19 06:00

Semin Respir Crit Care Med. 2022 Dec 19. doi: 10.1055/s-0042-1758734. Online ahead of print.

NO ABSTRACT

PMID:36535664 | DOI:10.1055/s-0042-1758734

Categories: Literature Watch

Respiratory Viruses and Cystic Fibrosis

Mon, 2022-12-19 06:00

Semin Respir Crit Care Med. 2022 Dec 19. doi: 10.1055/s-0042-1758728. Online ahead of print.

NO ABSTRACT

PMID:36535663 | DOI:10.1055/s-0042-1758728

Categories: Literature Watch

The experience of living with and managing cystic fibrosis related diabetes: a qualitative review

Mon, 2022-12-19 06:00

J Res Nurs. 2022 Dec;27(8):735-753. doi: 10.1177/17449871221116970. Epub 2022 Nov 4.

NO ABSTRACT

PMID:36530741 | PMC:PMC9755567 | DOI:10.1177/17449871221116970

Categories: Literature Watch

Commentary: The experience of living with and managing cystic fibrosis related diabetes: a qualitative review

Mon, 2022-12-19 06:00

J Res Nurs. 2022 Dec;27(8):754-756. doi: 10.1177/17449871221122836. Epub 2022 Nov 4.

NO ABSTRACT

PMID:36530740 | PMC:PMC9755572 | DOI:10.1177/17449871221122836

Categories: Literature Watch

Patient-derived cell models for personalized medicine approaches in cystic fibrosis

Sun, 2022-12-18 06:00

J Cyst Fibros. 2022 Dec 16:S1569-1993(22)01419-9. doi: 10.1016/j.jcf.2022.11.007. Online ahead of print.

NO ABSTRACT

PMID:36529661 | DOI:10.1016/j.jcf.2022.11.007

Categories: Literature Watch

Gene transfection using branched cationic amphiphilic compounds for an aerosol administration in cystic fibrosis context

Sun, 2022-12-18 06:00

Int J Pharm. 2022 Dec 15:122491. doi: 10.1016/j.ijpharm.2022.122491. Online ahead of print.

NO ABSTRACT

PMID:36529361 | DOI:10.1016/j.ijpharm.2022.122491

Categories: Literature Watch

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